Primary Ewing’s Sarcoma/Primitive Neuroectodermal Tumor of of Kidney - a Diagnostic Dilemma
نویسندگان
چکیده
Among the group of small round cell tumors of kidney Ewing's sarcoma/PNET is a very rare entity which has aggressive clinical course. We report a case of renal mass in 24 years old male which was histologically diagnosed as small round cell tumor of kidney. Arrangement of the malignant cell along with vascular network in a filigree pattern was suspicious for a diagnosis of Ewing's sarcoma/PNET which was confirmed by positivity of CD 99 immunohistochemically. Thus careful histological observation and immunohistochemical stains can give the proper diagnosis of primary Ewing's sarcoma/PNET thus removing the diagnostic dilemma in the group of small round cell tumors.
منابع مشابه
Breast Ewing Sarcoma/Primitive Neuroectodermal Tumor: A Case Report and a Review of the Literature
Extraskeletal Ewing’s Sarcoma is a rare soft tissue tumor that is morphologically indistinguishable from the more common Ewing’s sarcoma of the bone. Primitive Ewing’s sarcoma of the breast is exceptionally reported. We present the case of a 26-year-old woman with Ewing sarcoma/PNET diagnosed by molecular biology showing the specific t ranscr ipt of Ewing/ per ipheral pr imi t ive neuroectoderm...
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